A CASE OF FULMINANT ANCA-NEGATIVE WEGENER’S GRANULOMATOSIS WITH PRIMARY ENT INVOLVEMENT
DOI: https://doi.org/10.29296/25877305-2018-01-25
Issue:
1
Year:
2018
The paper describes a rare case of ANCA-negative Wegener's granulomatosis with a severe, fulminant course, which is manifested by primary ENT involvement.
Keywords:
rheumatology
Wegener’s granulomatosis
granulomatosis with polyangiitis
antineutrophil cytoplasmic antibodies (ANCA)
References:
- Allen S., Harvey C. Imaging of Wegener’s granulomatosis // Br. J. Radiol. – 2007; 80: 757–65.
- Mohammad A., Jacobsson L., Westman K. et al. Incidence and survival rates in Wegener’s granulomatosis, microscopic polyangiitis, Churg-Strauss syndrome and polyarteritisnodosa // Rheumatology (Oxford). – 2009; 12: 1560–5.
- Leavitt R., Fauci A., Bloch D. et. al. The American College of Rheumatology 1990 criteria for the classification of Wegener’s granulomatosis // Arthritis Rheum. – 1990; 33: 1101–7.
- Zubkova L.L., Baldanova I.R., Borhonova I.V. i dr. Granulematoz Vegenera (sluchaj iz praktiki) // Vestn. Burjatskogo gos. universiteta. – 2009; 12: 99–101.
- Kashiwagi T., Hayama N., Fujita E. et al. A case of (double) ANCA-negative granulomatosis with polyangiitis (Wegener’s) // CEN Case Reports – 2012; 1: 104–11.
- Savige J., Pollock W., Trevisin M. What do antineutrophil cytoplasmic antibodies (ANCA) tell us? // Best Pract. Res. Clin. Rheumatol. – 2005; 19 (2): 263–76.
- Hagen E., Daha M., Hermans J. et al. Diagnostic value of standardized assays for anti-neutrophil cytoplasmic antibodies in idiopathic systemic vasculitis. EC/BCR Project for ANCA Assay Standardization // Kidney Int. – 1998; 53 (3): 743–53.
- Hoffman G., Specks U. Antineutrophil cytoplasmic antibodies // Arthritis Rheum. – 1998; 41 (9): 1521–37.
- Pagnoux C., Wolter N. Vasculitis of the upper airways // Swiss. Med. Wkly. – 2012; 142: 13541.